Indicadores Socio-Emocionales del Espectro del Autismo en Individuos con Síndrome de Williams

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Maria Cristina Triguero Veloz Teixeira
Gisele da Silva Baraldi
Deisy Ribas Emerich
Mathias Levy de Wolinsk Miklos
Naiara Adorna da Silva
Regina Luísa de Freitas Marino
Chong Ae Kim
Rachel Sayuri Honjo
Décio Brunoni
Ana Alexandra Caldas Osório

Resumen

El Síndrome de Williams (SW) es una enfermedad genética causada por la delección de múltiplos genes en el cromosoma 7. Evidencias clínicas alertan para indicadores de afectaciones socio?emocionales compatibles con Trastorno del Espectro del Autismo (TEA). El objetivo del estudio fue identificar indicadores socio?emocionales y conductuales compatibles con Autismo en personas con SW. La muestra fue compuesta por 30 individuos con diagnóstico de SW y 22 con TEA. Los instrumentos de colecta de datos fueron Inventario de Conductas Autisticos (Autism Behavior Checklist – ABC); y Cuestionario de Conducta y Comunicación Social (Autism Screening Questionnaire – ASQ), respondidos por los respectivos cuidadores. Fue conducido un análisis discriminante (modelo Step Wise) para diferenciación de los grupos a partir de los itens de los inventarios ABC y ASQ. El grupo de personas con SW presentó un número expresivo de señales de alteraciones socio?emocionales, comunicativas y de conducta compatibles con Autismo que predominaron en la fase de los cuatro a cinco años de edad.

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Desarrollo Humano

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